Mitochondrial Diseases - Patrick Lestienne

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Sommaire:
Introduction.- Mitochondrial DNA Inheritance in Mammals.- Molecular Basis of Mitochondrial DNA Diseases.- Structural Studies of Human Mitochondrial tRNA.- Structure, Function and Pathology of Complex I.- Complex II or Succinate: Quinone Oxidoreductase and Pathology.- The bc1 Complex in the Mitochondrial Respiratory Chain.- Cytochrome c Oxidase and Mitochondrial Pathology.- ATPase-ATPsynthase and Mitochondrial Pathology.- Physiology and Pathophysiology of the Mitochondrial ADP/ATP Carrier.- The Normal and Pathological Structure , Function and Expression of Mitochondrial Creatine Kinase.- Pyruvate Dehydrogenase Deficiencies.- Electrochemical Gradient and Mitochondrial DNA in Living Cells.- A Heteroplasmic Strain of D. subobscura: An Animal Model of Mitochondrial Genome Rearrangements.- Stability of the Mitochondrial Genome of Podospora anserina and its Genetic Control.- The Control of Ageing and Mitochondria.- Roles of Mitochondria in Apoptosis.- The Triiodothyronine Mitochondrial Pathway.- Cytoskeleton-Mitochondrial Interactions.- NADH Brain Determination by Micromeasurements of a Laser Induced Fluorescence in the Rat.- Allotopic Expression of Mitochondrial Genes: Further Steps in the Evolution of Eukaryotic Cells and Therapeutic Strategy.- Import of tRNA into Yeast Mitochondria: Experimental Approaches and Possible Applications.- The Import of Cytosolic tRNA into Plant Mitochondria.- Plant Cytoplasmic Male Sterility: A Mitochondrial Pathology and Its Biotechnological Application.- Histopathology of Skeletal Muscle Mitochondria.- Enzymatic and Polarographic Measurements of the Respiratory Chain Complexes.- Mitochondrial DNA Analysis.-